CNS involvement and treatment with interferon-α are independent prognostic factors in Erdheim-Chester disease: a multicenter survival analysis of 53 patients

Arnaud, Laurent; Hervier, B.; Néel, A.; Hamidou, M.; Kahn, Jean‐Emmanuel; Wechsler, B.; Pérez‐Pastor, Gemma; Blomberg, Bjørn; Fuzibet, J.G.; Dubourguet, François; Marinho, António; Magnette, Catherine; Noël, Violaine; Pavic, Michel; Casper, Jochen; Beucher, Anne-Bérangère; Costedoat‐Chalumeau, N.; Aaron, Laurent; Salvatierra, Juan; Graux, Carlos; Cacoub, P.; Delcey, V.; Dechant, Claudia; Bindi, Pascal; Herbaut, C; Graziani, G.; Amoura, Zahir; Haroche, Julien

doi:10.1182/blood-2010-06-294108

Public

CNS involvement and treatment with interferon-α are independent prognostic factors in Erdheim-Chester disease: a multicenter survival analysis of 53 patients

Published in Blood • Jan 15, 2011

Authors:

Laurent Arnaud

B. Hervier

A. Néel

Abstract

Erdheim-Chester disease (ECD) is a rare form of non-Langerhans histiocytosis, with noncodified therapeutic management and high mortality. No treatment has yet been shown to improve survival in these patients. We conducted a multicenter prospective observational cohort study to assess whether extrask...

Subject

Erdheim–Chester disease

Medicine

Internal medicine

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