Use of modified cornstarch therapy to extend fasting in glycogen storage disease types Ia and Ib.

E Correia, Catherine; Bhattacharya, Kaustuv; J Lee, Philip; J Shuster, Jonathan; W Theriaque, Douglas; N Shankar, Meena; Peter A Smit, G; A Weinstein, David

doi:10.3945/ajcn.2008.26352

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Use of modified cornstarch therapy to extend fasting in glycogen storage disease types Ia and Ib.

Shared by NobleBlocks on Nov 1, 2008 • 12:00 AM UTC

Authors:

Catherine E Correia

Kaustuv Bhattacharya

Philip J Lee

Abstract

BACKGROUND: Type I glycogen storage disease (GSD) is caused by a deficiency of glucose-6-phosphatase resulting in severe fasting hypoglycemia. OBJECTIVE: We compared the efficacy of a new modified starch with the currently used cornstarch therapy in patients with type Ia and Ib GSD. DESIGN: This was...

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