Connective Tissue Disease–associated Pulmonary Arterial Hypertension in the Modern Treatment Era

Condliffe, Robin; G. Kiely, David; J. Peacock, Andrew; A. Corris, Paul; Simon R. Gibbs, J.; Vrapi, Florenc; Das, Clare; A. Elliot, Charlie; Johnson, Martin; DeSoyza, Julia; Torpy, Chantal; Goldsmith, Kim; Hodgkins, Denise; J. Hughes, Rodney; Pepke-Zaba, Joanna; Gerry Coghlan, J.

doi:10.1164/rccm.200806-953oc

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Connective Tissue Disease–associated Pulmonary Arterial Hypertension in the Modern Treatment Era

Shared by NobleBlocks on Jan 1, 2009 • 12:00 AM UTC

Authors:

Robin Condliffe

David G. Kiely

Andrew J. Peacock

Abstract

Abstract Rationale Pulmonary arterial hypertension in association with connective tissue disease (CTD-PAH) has historically had a poor prognosis, with a 1-year survival rate among patients with systemic sclerosis–associated pulmonary arterial hypertension (SSc-PAH) of 45%. However, more therapies ha...

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